{
  "name": "Kawasaki Disease",
  "slug": "kawasaki-disease",
  "url": "https://nursingplex.com/care-plans/kawasaki-disease",
  "category": "Hematologic & Lymphatic",
  "summary": "Pediatric vasculitis with fever and coronary risk; IVIG, aspirin and comfort care.",
  "nursing_diagnoses": [
    "Hyperthermia",
    "Acute pain",
    "Risk for decreased cardiac output"
  ],
  "overview": [
    "Kawasaki disease is an acute systemic vasculitis of unknown cause that mainly strikes children under 5. Its importance is entirely in the coronary arteries: without treatment, roughly a quarter of children develop coronary artery aneurysms, making it the leading cause of acquired heart disease in children in developed countries. Timely IV immunoglobulin within the first 10 days of fever cuts that risk dramatically.",
    "Diagnosis is clinical. A fever lasting five or more days that does not respond to antipyretics or antibiotics, plus at least four of: bilateral non-exudative conjunctivitis, a strawberry tongue with cracked red lips, polymorphous rash, erythema and swelling of the hands and feet, and cervical lymphadenopathy. The child is characteristically extremely irritable — often described as the most irritable child on the unit.",
    "The illness moves through three phases: an acute febrile phase of 1–2 weeks, a subacute phase where fever resolves but the platelet count soars and the skin of the fingers and toes peels — the highest-risk window for aneurysm and thrombosis — and a convalescent phase lasting until inflammatory markers normalize, typically 6–8 weeks."
  ],
  "key_facts": [
    {
      "label": "Treatment window",
      "text": "IVIG plus aspirin within 10 days of fever onset markedly reduces coronary aneurysm risk."
    },
    {
      "label": "The aspirin exception",
      "text": "This is one of the few pediatric conditions where aspirin is indicated: high-dose anti-inflammatory during fever, then low-dose antiplatelet."
    },
    {
      "label": "Subacute clue",
      "text": "Peeling (desquamation) of fingers and toes with a very high platelet count marks the peak thrombosis risk period."
    },
    {
      "label": "Vaccine caution",
      "text": "Delay live vaccines (MMR, varicella) for 11 months after IVIG; the antibodies blunt the response."
    },
    {
      "label": "Monitoring",
      "text": "Echocardiogram at diagnosis, at 2 weeks and at 6–8 weeks to track coronary arteries."
    }
  ],
  "nursing_priorities": [
    "Give IVIG within the 10-day window and monitor the infusion closely.",
    "Detect and monitor for cardiac complications.",
    "Manage fever, pain and extreme irritability.",
    "Protect fragile skin and mucous membranes.",
    "Maintain hydration when the mouth is painful.",
    "Teach the family long-term follow-up and aspirin safety."
  ],
  "assessment": {
    "subjective": [
      "Parents report a high fever unresponsive to acetaminophen or ibuprofen for five or more days",
      "Extreme irritability and inconsolability out of proportion to other findings",
      "Refusal to eat or drink because of sore mouth and lips",
      "Joint pain and refusal to walk or bear weight"
    ],
    "objective": [
      "Fever ≥5 days, often 39–40 °C, spiking and unresponsive to antipyretics",
      "Bilateral bulbar conjunctival injection without exudate",
      "Strawberry tongue, dry cracked fissured lips, diffuse oral erythema",
      "Polymorphous truncal rash, sometimes prominent in the diaper area",
      "Erythema and firm edema of the palms and soles; later periungual peeling",
      "Unilateral cervical lymph node greater than 1.5 cm",
      "Elevated ESR, CRP and white count; thrombocytosis in the subacute phase; sterile pyuria",
      "Tachycardia out of proportion to fever, gallop rhythm, or signs of myocarditis"
    ],
    "related_factors": [
      "Systemic vasculitis of medium-sized arteries, especially the coronaries",
      "Prolonged high fever with increased metabolic and fluid demand",
      "Painful oral mucositis limiting intake",
      "Skin inflammation, edema and desquamation",
      "Thrombocytosis and hypercoagulability in the subacute phase"
    ]
  },
  "goals": [
    "The child will become afebrile within 36 hours of IVIG completion.",
    "The child will maintain adequate hydration with appropriate urine output and moist mucous membranes.",
    "The child will show no signs of cardiac compromise: normal rate for age, no gallop, no respiratory distress.",
    "The child will have intact skin with peeling areas managed and free of infection.",
    "The child will appear comfortable and consolable with fewer irritability episodes.",
    "The parents will describe aspirin dosing, follow-up echocardiograms and vaccine timing before discharge."
  ],
  "interventions": [
    {
      "title": "1. Administering IVIG safely",
      "points": [
        "Obtain baseline vital signs and infuse IVIG at the prescribed slow rate, increasing only per protocol.",
        "Monitor vital signs frequently during the infusion — every 15 minutes initially — for fever, chills, rash, headache, flushing or hypotension.",
        "Assess for fluid overload: this is a large volume in a child who may already have myocarditis. Watch for tachypnea, crackles, gallop and rising weight.",
        "Stop the infusion and notify the provider for signs of reaction; restart at a slower rate only as ordered.",
        "Anticipate a second IVIG dose if fever persists or recurs beyond 36 hours after the first."
      ]
    },
    {
      "title": "2. Monitoring the heart",
      "points": [
        "Assess heart rate, rhythm, perfusion and blood pressure at least every 4 hours; report a gallop, murmur or persistent tachycardia after the fever resolves.",
        "Watch for heart failure signs: tachypnea, retractions, hepatomegaly, poor feeding, sweating with feeds and decreasing urine output.",
        "Prepare the family for serial echocardiograms and explain what each one is checking.",
        "Report chest pain, pallor, unexplained vomiting or a sudden change in behavior, which in the subacute phase can indicate coronary thrombosis."
      ]
    },
    {
      "title": "3. Managing fever, pain and irritability",
      "points": [
        "Administer high-dose aspirin during the febrile phase and transition to low-dose antiplatelet aspirin as prescribed after defervescence.",
        "Cluster care and keep the environment quiet and dim; the irritability is part of the disease and cannot be soothed away, but overstimulation makes it worse.",
        "Encourage parents to hold and rock the child and to bring familiar comfort items.",
        "Use cool cloths and light clothing rather than aggressive cooling measures that cause shivering.",
        "Handle painfully swollen hands and feet gently and support them on pillows."
      ]
    },
    {
      "title": "4. Skin, mouth and hydration care",
      "points": [
        "Apply unscented emollients to dry skin and lubricating ointment to cracked lips; do not peel loose skin, allow it to separate.",
        "Provide gentle mouth care with soft swabs and offer cool, soft, bland foods and fluids — popsicles, gelatin, milkshakes — rather than acidic juices.",
        "Track intake and output and daily weight; offer small volumes very frequently.",
        "Inspect skin folds, the diaper area and desquamating fingers and toes for breakdown or secondary infection.",
        "Keep nails short and consider soft mittens if the child scratches."
      ]
    },
    {
      "title": "5. Family teaching and follow-up",
      "points": [
        "Explain the three phases so parents are not alarmed when peeling begins after the fever resolves.",
        "Teach exact aspirin dosing and the Reye syndrome caution: contact the provider if the child develops influenza or varicella while taking aspirin, and ensure annual influenza vaccination.",
        "Explain that live vaccines must be delayed about 11 months after IVIG and give a written date.",
        "Stress that follow-up echocardiograms are essential even if the child looks completely well.",
        "Advise avoiding contact sports if coronary aneurysms are present and the child is on antiplatelet therapy."
      ]
    }
  ],
  "patient_teaching": [
    "Give aspirin exactly as prescribed and never stop it early; call before giving any other medication.",
    "Call the provider if your child develops chickenpox or flu symptoms while taking aspirin.",
    "Expect peeling of the fingers and toes 1–2 weeks after the fever — this is normal and not an infection.",
    "Report return of fever, irritability, chest pain, unusual sleepiness, pallor or difficulty breathing immediately.",
    "Keep all cardiology appointments and echocardiograms, even when your child seems fully recovered.",
    "Delay live vaccines for about 11 months after IVIG and keep the influenza vaccine current.",
    "Offer soft, cool foods and plenty of fluids while the mouth is sore."
  ]
}